Vasculitis necrotizantes sistémicas, vasculitis asociadas a ANCA
ISSN: 0304-5412
Argitalpen urtea: 2013
Zenbakien izenburua: Enfermedades del sistema inmune (VI): vasculitis y miopatías inflamatorias
Saila: 11
Zenbakia: 33
Orrialdeak: 2021-2028
Mota: Artikulua
Beste argitalpen batzuk: Medicine: Programa de Formación Médica Continuada Acreditado
Garapen Iraunkorreko Helburuak
Laburpena
Systemic necrotizing vasculitides are a non homogeneous group of diseases defined by clinical symptoms of multivisceral involvement that are the consequence of severe inflammation of the arterial wall and histologically for the presence of fibrinoid necrosis. The polyarteritis nodosa (PAN) is a systemic vasculitides that affect the small-and medium-sized arteries. Antineutrophil cytoplasmatic antibody (ANCAs)-associated vasculitides include granulomatosis with polyangiitis (GPA), microscopic polyangiitis (MPA), and the allergic granulomatosis and angiitis or Churg Strauss syndrome (CSS) that affect essentially small-sized arteries. GPA and MPA vasculitides have a common renal involvement (pauci-immune crescentic glomerulonephritis) and share treatment and evolution. The SCS has a different presentation and prognosis compared with the other ANCAs.